Haemodynamically proven pulmonary hypertension in a patient with GATA2 deficiency-associated pulmonary alveolar proteinosis and fibrosis

Sébastien Sanges; Anne Prévotat; Marie Fertin; Louis Terriou; Guillaume Lefèvre; Bruno Quesnel; Pierre-Yves Hatron; Éric Hachulla; Marie-Christine Copin; David Launay

doi:10.1183/13993003.00178-2017

Haemodynamically proven pulmonary hypertension in a patient with GATA2 deficiency-associated pulmonary alveolar proteinosis and fibrosis

Eur Respir J. 2017 May 11;49(5):1700178. doi: 10.1183/13993003.00178-2017. Print 2017 May.

Authors

Sébastien Sanges^{1

2

3

4}, Anne Prévotat⁵, Marie Fertin⁶, Louis Terriou^{1

2

3

4}, Guillaume Lefèvre^{1

2

3

4

7}, Bruno Quesnel⁸, Pierre-Yves Hatron^{1

3

4}, Éric Hachulla^{1

2

3

4}, Marie-Christine Copin⁹, David Launay^{10

2

3

4}

Affiliations

¹ Univ. Lille, INSERM U995 - LIRIC - Lille Inflammation Research International Center, Lille, France.
² INSERM, U995, Lille, France.
³ CHU Lille, Département de Médecine Interne et Immunologie Clinique, Lille, France.
⁴ Centre National de Référence Maladies Systémiques et Auto-immunes Rares (Sclérodermie Systémique), Lille, France.
⁵ CHU Lille, Service de Pneumologie, Lille, France.
⁶ CHU Lille, Service de Cardiologie, Lille, France.
⁷ CHU Lille, Institut d'Immunologie, Lille, France.
⁸ CHU Lille, Service des Maladies du Sang, Lille, France.
⁹ CHU Lille, Institut de Pathologie, Lille, France.
¹⁰ Univ. Lille, INSERM U995 - LIRIC - Lille Inflammation Research International Center, Lille, France david.launay@univ-lille2.fr.

PMID: 28495695
DOI: 10.1183/13993003.00178-2017

No abstract available

Publication types

Letter
Comment

MeSH terms

GATA2 Transcription Factor
Humans
Hypertension, Pulmonary*
Immunologic Deficiency Syndromes
Pulmonary Alveolar Proteinosis*

Substances

GATA2 Transcription Factor
GATA2 protein, human