Liver disease in cystic fibrosis presents as non-cirrhotic portal hypertension

J Cyst Fibros. 2017 Sep;16(5):e11-e13. doi: 10.1016/j.jcf.2017.03.006. Epub 2017 Mar 25.
No abstract available

Keywords: Calcification; Nodular regenerative hyperplasia; Obliterative venopathy; Phlebosclerosis; Presinusoidal portal hypertension.

Publication types

  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Biopsy / methods
  • Cystic Fibrosis / complications*
  • Cystic Fibrosis / diagnosis
  • Female
  • Hemodynamics
  • Humans
  • Hypertension, Portal* / diagnosis
  • Hypertension, Portal* / etiology
  • Hypertension, Portal* / physiopathology
  • Liver / pathology*
  • Liver Circulation
  • Liver Cirrhosis* / diagnosis
  • Liver Cirrhosis* / etiology
  • Liver Cirrhosis* / physiopathology
  • Liver Function Tests / methods
  • Male
  • Portal System / physiopathology
  • Severity of Illness Index