Objective: The inflammatory myofibroblastic tumor (IMT) is a neoplasia with intermediate biological potential, infrequent, with an unpredictable clinical prognosis and a low recurrence rate after an effective treatment. We report two cases of IMT with genitourinary localization, being this entit's publications infrequent. Both presented with little symptomatology, leading to multiple differential diagnosis. The surgical treatment was chosen and pathologic result confirmed the diagnosis.
Conclusion: This entity must be considered as a true malignant neoplasm with aggressive local behavior. The gold standard management is complete surgical resection, with low recurrence rate after it. A new oncological monitoring scheme is proposed, upon the lack of an active surveillance algorithm after treatment.