Restrictive Lung Disease in the Cu/Zn Superoxide-Dismutase 1 G93A Amyotrophic Lateral Sclerosis Mouse Model

Am J Respir Cell Mol Biol. 2017 Mar;56(3):405-408. doi: 10.1165/rcmb.2016-0258LE.
No abstract available

Publication types

  • Letter
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amyotrophic Lateral Sclerosis* / enzymology
  • Amyotrophic Lateral Sclerosis* / genetics
  • Animals
  • Humans
  • Lung Diseases* / enzymology
  • Lung Diseases* / genetics
  • Mice
  • Mice, Mutant Strains
  • Superoxide Dismutase* / genetics
  • Superoxide Dismutase* / metabolism

Substances

  • SOD1 G93A protein
  • Superoxide Dismutase