A congenital diverticulum of the left ventricular apex manifested by stroke and recurrent ventricular tachycardia

Cardiovasc Pathol. 2017 May-Jun:28:3-6. doi: 10.1016/j.carpath.2017.01.009. Epub 2017 Feb 4.

Abstract

Ventricular outpouchings include acquired abnormalities (aneurysms and pseudoaneurysms) and congenital ventricular diverticula (CVD). CVD represent rare cardiac pathologies. Although CVD is often associated with other cardiac and extracardiac congenital anomalies, it can also be incidentally observed in otherwise healthy subjects. CVD may lead to significant morbidity and even have lethal consequences. We describe a case of arrhythmogenic left ventricle (LV) apical CVD revealed by cardiac magnetic resonance imaging (CMRI) after being initially overlooked by echocardiography. The paper includes the review of the literature also. This clinical case highlights the possible association of this pathology with recurrent ventricular tachycardia and stroke, and illustrates the importance of multimodal imaging approach in differential diagnosis.

Keywords: Congenital heart disease; Diverticulum; Left ventricle; Ventricular tachycardia.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Diverticulum / congenital*
  • Diverticulum / diagnostic imaging
  • Diverticulum / physiopathology
  • Diverticulum / surgery
  • Echocardiography, Doppler, Pulsed
  • Electrophysiologic Techniques, Cardiac
  • Fibrosis
  • Heart Defects, Congenital / complications*
  • Heart Defects, Congenital / diagnostic imaging
  • Heart Defects, Congenital / physiopathology
  • Heart Defects, Congenital / surgery
  • Heart Ventricles / abnormalities*
  • Heart Ventricles / diagnostic imaging
  • Heart Ventricles / physiopathology
  • Heart Ventricles / surgery
  • Humans
  • Magnetic Resonance Imaging
  • Predictive Value of Tests
  • Recurrence
  • Stroke / diagnosis
  • Stroke / etiology*
  • Tachycardia, Ventricular / diagnosis
  • Tachycardia, Ventricular / etiology*
  • Tachycardia, Ventricular / physiopathology
  • Treatment Outcome