Progressive hearing loss in Usher's syndrome

Ann Otol Rhinol Laryngol. 1989 Nov;98(11):863-6. doi: 10.1177/000348948909801106.

Abstract

In 18 patients with Usher's syndrome, progressive hearing loss was verified audiologically in eight cases. Despite poor auditory threshold values and low speech discrimination scores, there was only one patient who could not communicate with speech. The possibility of hearing impairment being mainly progressive in Usher's syndrome is discussed.

MeSH terms

  • Adolescent
  • Adult
  • Audiometry, Pure-Tone
  • Auditory Threshold
  • Female
  • Hearing Disorders / diagnosis
  • Hearing Disorders / genetics*
  • Humans
  • Male
  • Middle Aged
  • Retinitis Pigmentosa / genetics*
  • Speech Discrimination Tests
  • Syndrome