Extracorporeal membrane oxygenation rescue in adolescent with bronchiolitis obliterans-organizing pneumonia like Wegener's granulomatosis

Clin Case Rep. 2016 Dec 17;5(1):29-34. doi: 10.1002/ccr3.752. eCollection 2017 Jan.

Abstract

We report a 17-year-old woman with bronchiolitis obliterans-organizing pneumonia (BOOP)-like granulomatosis with polyangiitis developing severe airway obliterations. Pending age, phase and grade of autoimmune treatment, and offering ECMO treatment may be crucial for survival but occasionally preface futility. ECMO-treated patient with BOOP-like GPA has never been described before.

Keywords: Extracorporeal membrane oxygenation; Wegener's granulomatosis; granulomatosis with polyangiitis.

Publication types

  • Case Reports