Der Zytokinsturm – eine Komplikation des adulten Morbus Still

Praxis (Bern 1994). 2016;105(25):1503-1506. doi: 10.1024/1661-8157/a002562.
[Article in German]
No abstract available

Keywords: Hyperferritinämie; Makrophagen-Aktivierungs-Syndrom; Sturm; Zytokin; adult onset Still’s disease; adulter Morbus Still; cytokine storm; hyperferritinemia; macrophage activation syndrome.

Publication types

  • Case Reports

MeSH terms

  • Administration, Inhalation
  • Adult
  • Antibodies, Monoclonal, Humanized / therapeutic use
  • Cyclosporine / therapeutic use
  • Cytokines / blood*
  • Dose-Response Relationship, Drug
  • Drug Hypersensitivity / immunology
  • Drug Therapy, Combination
  • Female
  • Ferritins / blood
  • Humans
  • Lymphocyte Activation / drug effects
  • Lymphocyte Activation / immunology
  • Macrophage Activation Syndrome / diagnosis
  • Macrophage Activation Syndrome / drug therapy
  • Macrophage Activation Syndrome / immunology
  • Pentamidine / therapeutic use
  • Prednisone / therapeutic use
  • Recurrence
  • Still's Disease, Adult-Onset / complications*
  • Still's Disease, Adult-Onset / diagnosis
  • Still's Disease, Adult-Onset / drug therapy
  • Still's Disease, Adult-Onset / immunology
  • T-Lymphocytes / drug effects
  • Trimethoprim, Sulfamethoxazole Drug Combination / adverse effects
  • Trimethoprim, Sulfamethoxazole Drug Combination / therapeutic use

Substances

  • Antibodies, Monoclonal, Humanized
  • Cytokines
  • Pentamidine
  • Trimethoprim, Sulfamethoxazole Drug Combination
  • Cyclosporine
  • Ferritins
  • tocilizumab
  • Prednisone