An Adult Case of Unicommissural Unicuspid Aortic Valve Diagnosed Based on the Intraoperative Findings

Intern Med. 2016;55(18):2643-8. doi: 10.2169/internalmedicine.55.6861. Epub 2016 Sep 15.

Abstract

We herein report an adult case of unicommissural unicuspid aortic valve (UAV). A 59-year-old man, who was noted to have a cardiac murmur at 31 years of age, was admitted to our hospital due to acute heart failure. Severe calcification in the aortic valve with severe low-flow/low-gradient aortic stenosis and moderate aortic regurgitation was observed and thought to be the cause of heart failure, however, the etiology of aortic valve dysfunction was not clear. Aortic valve replacement was subsequently performed, and unicommissural UAV was diagnosed according to the intraoperative findings. UAV is very rare congenital aortic valve disease which is rarely diagnosed preoperatively.

Publication types

  • Case Reports

MeSH terms

  • Aortic Valve / abnormalities*
  • Aortic Valve / diagnostic imaging
  • Aortic Valve / surgery
  • Aortic Valve Insufficiency / complications
  • Aortic Valve Insufficiency / diagnostic imaging*
  • Aortic Valve Insufficiency / physiopathology
  • Aortic Valve Stenosis / etiology
  • Aortic Valve Stenosis / physiopathology
  • Aortic Valve Stenosis / surgery*
  • Calcinosis / complications
  • Calcinosis / diagnostic imaging*
  • Calcinosis / physiopathology
  • Echocardiography, Transesophageal*
  • Heart Failure / complications
  • Heart Failure / physiopathology
  • Heart Failure / surgery*
  • Heart Valve Prosthesis / adverse effects
  • Heart Valve Prosthesis Implantation / methods*
  • Humans
  • Male
  • Middle Aged
  • Treatment Outcome