No abstract available
Keywords:
Autophagosome; Autophagy; Calpain; Motoneuron; Rapamycin; Spinal Muscular Atrophy; Survival motor neuron.
Publication types
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Research Support, Non-U.S. Gov't
MeSH terms
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Animals
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Animals, Newborn
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Autophagy / drug effects
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Autophagy / genetics
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Autophagy / physiology*
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Cell Survival / genetics
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Cell Survival / physiology
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Cells, Cultured
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Disease Models, Animal
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Embryo, Mammalian
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Enzyme Inhibitors / pharmacology
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Gene Expression Regulation, Developmental / drug effects
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Gene Expression Regulation, Developmental / genetics
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Gene Expression Regulation, Developmental / physiology
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Macrolides / pharmacology
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Mice
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Mice, Transgenic
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Motor Neurons / drug effects
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Motor Neurons / metabolism*
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Motor Neurons / ultrastructure
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Muscular Atrophy, Spinal / genetics
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Muscular Atrophy, Spinal / pathology*
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Nerve Growth Factors / pharmacology
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Nerve Tissue Proteins / genetics
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Nerve Tissue Proteins / metabolism*
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Sequestosome-1 Protein / metabolism
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Spinal Cord / cytology
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Spinal Cord / growth & development
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Survival of Motor Neuron 1 Protein / genetics
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Survival of Motor Neuron 1 Protein / metabolism
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Survival of Motor Neuron 2 Protein / genetics
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Survival of Motor Neuron 2 Protein / metabolism
Substances
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Enzyme Inhibitors
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Macrolides
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Nerve Growth Factors
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Nerve Tissue Proteins
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SMN2 protein, human
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SQSTM1 protein, human
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Sequestosome-1 Protein
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Smn1 protein, mouse
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Survival of Motor Neuron 1 Protein
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Survival of Motor Neuron 2 Protein
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bafilomycin A1