Medallion-Like Dermal Dendrocytic Hamartoma, Dermatofibrosarcoma Protuberans, and Adenosine Deaminase-Deficient Severe Combined Immunodeficiency

Pediatr Dermatol. 2016 May;33(3):359-60. doi: 10.1111/pde.12847.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Adenosine Deaminase / deficiency*
  • Agammaglobulinemia / diagnosis
  • Agammaglobulinemia / parasitology*
  • Biopsy, Needle
  • Child
  • Dermatofibrosarcoma / diagnosis
  • Dermatofibrosarcoma / pathology*
  • Diagnosis, Differential
  • Female
  • Hamartoma / diagnosis
  • Hamartoma / pathology*
  • Humans
  • Immunohistochemistry
  • Rare Diseases
  • Severe Combined Immunodeficiency / diagnosis
  • Severe Combined Immunodeficiency / parasitology*
  • Skin Neoplasms / diagnosis
  • Skin Neoplasms / pathology*

Substances

  • Adenosine Deaminase

Supplementary concepts

  • Severe combined immunodeficiency due to adenosine deaminase deficiency