Orbital tumour due rhinosinusal extension in a patient with Wegener's granulomatosis
Arch Soc Esp Oftalmol. 2016 Sep;91(9):442-5.
doi: 10.1016/j.oftal.2016.02.011.
Epub 2016 Mar 23.
[Article in
English,
Spanish]
Affiliations
- 1 Servicio de Oftalmología, Hospital Universitario Virgen del Rocío, Sevilla, España. Electronic address: fredy_771@hotmail.com.
- 2 Servicio de Oftalmología, Hospital Universitario Virgen del Rocío, Sevilla, España.
Abstract
Case report:
The case is presented of a 49 year-old woman with an orbital mass originating from the rhinosinus. She had a history of Wegener's granulomatosis, refractory to both biological and immunosuppressive therapy. Clinical examination showed proptosis, diplopia, and restriction of ocular movements.
Discussion:
Orbital mass resection was performed, due to its rapid growth, and lack of response to medical treatment.
Keywords:
Diplopia; Diplopía; Granulomatosis de Wegener; Orbital tumour; Proptosis; Rhinosinus tumour; Tumoración orbitaria; Tumoración rinosinusal; Wegener's granulomatosis.
Copyright © 2016 Sociedad Española de Oftalmología. Published by Elsevier España, S.L.U. All rights reserved.
MeSH terms
-
Combined Modality Therapy
-
Diplopia / etiology
-
Disease Progression
-
Drug Resistance
-
Ethmoid Sinus / diagnostic imaging*
-
Ethmoid Sinus / surgery
-
Exophthalmos / etiology
-
Female
-
Granuloma / complications
-
Granuloma / pathology*
-
Granulomatosis with Polyangiitis / complications
-
Granulomatosis with Polyangiitis / drug therapy
-
Granulomatosis with Polyangiitis / pathology*
-
Granulomatosis with Polyangiitis / surgery
-
Humans
-
Immunosuppressive Agents / therapeutic use
-
Middle Aged
-
Nasal Cavity / diagnostic imaging*
-
Orbital Diseases / diagnostic imaging
-
Orbital Diseases / pathology*
-
Orbital Diseases / surgery
-
Tomography, X-Ray Computed