Combined pleomorphic xanthoastrocytoma-ganglioglioma with BRAF V600E mutation: case report

J Neurosurg Pediatr. 2016 Jul;18(1):53-7. doi: 10.3171/2016.1.PEDS15558. Epub 2016 Mar 25.

Abstract

Combined pleomorphic xanthoastrocytoma (PXA) and ganglioglioma (GG) is an extremely rare tumor, with fewer than 20 cases reported. The authors report a case of combined PXA-GG in an 18-year-old man with a history of seizures. The tumor showed necrosis and the BRAF V600E mutation on histological examination, with no evidence of tumor recurrence 1 year after gross-total resection. The BRAF V600E mutation was present, which suggests that both cell lineages may share a common cellular origin.

Keywords: BRAF mutation; GFAP = glial fibrillary acidic protein; GG = ganglioglioma; PCR = polymerase chain reaction; PXA = pleomorphic xanthoastrocytoma; combined pleomorphic xanthoastrocytoma-ganglioglioma; ganglioglioma; oncology; pleomorphic xanthoastrocytoma.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Astrocytoma / diagnosis
  • Astrocytoma / genetics*
  • Astrocytoma / surgery
  • Brain Neoplasms / diagnosis
  • Brain Neoplasms / genetics*
  • Brain Neoplasms / surgery
  • Ganglioglioma / diagnosis
  • Ganglioglioma / genetics*
  • Ganglioglioma / surgery
  • Humans
  • Male
  • Mutation / genetics*
  • Proto-Oncogene Proteins B-raf / genetics*

Substances

  • BRAF protein, human
  • Proto-Oncogene Proteins B-raf