[Differential diagnosis of aortitis]

Rev Med Interne. 2016 Apr;37(4):256-63. doi: 10.1016/j.revmed.2016.02.002. Epub 2016 Mar 3.
[Article in French]

Abstract

Aortitis are mainly described in inflammatory disorders such as Takayasu arteritis, giant cell arteritis or Behçet's disease. Aortitis is sometimes qualified as idiopathic. However, differential diagnoses must be searched since they need specific interventions. Infectious aortitis should be ruled out first as its rapid evolution and short-term poor prognosis makes it a therapeutic emergency. Furthermore, rarer differential diagnoses should be known as they require specific care that might sometimes differ from the treatment of inflammatory aortitis, such as retroperitoneal fibrosis mostly idiopathic but also secondary to neoplasia or malignant hemopathies. IgG4 related disease, Erdheim-Chester disease and inflammatory abdominal aortic aneurysm due to atherosclerosis are other differential diagnoses to mention in the presence of aortitis in order to adapt patients' care consequently.

Keywords: Aneurysm; Anévrisme; Aortites infectieuses; Aortites inflammatoires; Fibrose rétropéritonéale; Infectious aortitis; Inflammatory aortitis; Retroperitoneal fibrosis.

Publication types

  • Review

MeSH terms

  • Aortitis / diagnosis*
  • Aortitis / etiology*
  • Behcet Syndrome / complications
  • Behcet Syndrome / diagnosis
  • Diagnosis, Differential
  • Erdheim-Chester Disease / complications
  • Erdheim-Chester Disease / diagnosis
  • Giant Cell Arteritis / complications
  • Giant Cell Arteritis / diagnosis
  • Humans
  • Immunoglobulin G / adverse effects
  • Syphilis, Cardiovascular / complications
  • Syphilis, Cardiovascular / diagnosis
  • Takayasu Arteritis / complications
  • Takayasu Arteritis / diagnosis
  • Tuberculosis, Cardiovascular / complications
  • Tuberculosis, Cardiovascular / diagnosis

Substances

  • Immunoglobulin G