Lung clearance index response in patients with CF with class III CFTR mutations

Thorax. 2016 May;71(5):476-7. doi: 10.1136/thoraxjnl-2015-207894. Epub 2016 Mar 4.
No abstract available

Keywords: Cystic Fibrosis.

Publication types

  • Observational Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Alleles
  • Aminophenols / therapeutic use*
  • Cystic Fibrosis / diagnosis
  • Cystic Fibrosis / drug therapy*
  • Cystic Fibrosis / genetics*
  • Cystic Fibrosis Transmembrane Conductance Regulator / drug effects*
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Forced Expiratory Volume / drug effects
  • Humans
  • Maximal Midexpiratory Flow Rate
  • Mutation*
  • Quinolones / therapeutic use*
  • Saline Solution, Hypertonic / therapeutic use
  • Severity of Illness Index
  • Spirometry
  • Treatment Outcome

Substances

  • Aminophenols
  • Quinolones
  • Saline Solution, Hypertonic
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • ivacaftor