Left bronchial compression and pulmonary hypertension related to anomalous right pulmonary artery

Cardiol Young. 2016 Jun;26(5):999-1001. doi: 10.1017/S104795111600010X. Epub 2016 Feb 22.

Abstract

Anomalous origin of a pulmonary artery from the ascending aorta is a congenital defect that can be complicated by pulmonary arterial hypertension, typically due to vascular disease if the anomaly is left uncorrected past 6 months of age. We describe a unique case of severe pulmonary arterial hypertension with this defect in a 1-month-old infant unexpectedly caused instead by bronchial compression from her dilated left pulmonary artery.

Keywords: Anomalous origin of one pulmonary artery from the aorta; heart failure; infant; pulmonary arterial hypertension; pulmonary vascular disease.

Publication types

  • Case Reports

MeSH terms

  • Aorta / abnormalities*
  • Bronchial Diseases / diagnostic imaging*
  • Computed Tomography Angiography
  • Echocardiography
  • Female
  • Humans
  • Hypertension, Pulmonary / etiology*
  • Infant
  • Pulmonary Artery / abnormalities*
  • Vascular Malformations / complications*
  • Vascular Malformations / diagnostic imaging*