[Histiocytoid cardiomyopathy concurrent with noncompact myocardium, myocarditis, and pericarditis]

Arkh Patol. 2015 Nov-Dec;77(6):45-49. doi: 10.17116/patol201577645-49.
[Article in Russian]

Abstract

The paper presents a practical case of histiocytoid cardiomyopathy concurrent with noncompact myocardium, atrial septal defects, myocarditis, and pericarditis in an 8-month-old girl, by describing their clinical presentations and a morphological examination.

Представлено наблюдение из практики - сочетание гистиоцитоидной кардиомиопатии с некомпактным миокардом, дефектами межпредсердной перегородки, миокардитом и перикардитом у девочки 8 мес с описанием клиники и морфологического исследования.

MeSH terms

  • Cardiomyopathies / congenital*
  • Cardiomyopathies / etiology
  • Cardiomyopathies / physiopathology
  • Electron Transport Complex III / deficiency*
  • Female
  • Heart Ventricles / physiopathology
  • Humans
  • Infant
  • Myocarditis / physiopathology*
  • Myocardium / pathology
  • Myocardium / ultrastructure*
  • Pericarditis / physiopathology*
  • Purkinje Cells / pathology
  • Purkinje Cells / ultrastructure

Substances

  • Electron Transport Complex III

Supplementary concepts

  • Cardiomyopathy, infantile histiocytoid