Unusual Outcome of a Right Ventricular Rhabdomyoma in an Infant

World J Pediatr Congenit Heart Surg. 2016 May;7(3):397-9. doi: 10.1177/2150135115593133. Epub 2016 Jan 21.

Abstract

Rhabdomyomas are the most common benign cardiac tumors. They may often be associated with tuberous sclerosis. In many cases, cardiac rhabdomyomas undergo spontaneous regression. Here, we report the unusual case of an infant with a large nonobstructive right ventricular rhabdomyoma at birth and at four months of age, which subsequently caused severe right ventricle outflow tract obstruction at six months of age, prompting surgery to remove the tumor. Close monitoring should be done in infants with large nonobstructive cardiac rhabdomyomas.

Keywords: cardiac tumors (includes myxoma; echocardiography; emergency; infant; metastases); primary; surgery.

Publication types

  • Case Reports

MeSH terms

  • Disease Progression
  • Heart Neoplasms / complications
  • Heart Neoplasms / diagnostic imaging*
  • Heart Neoplasms / surgery
  • Heart Ventricles / pathology
  • Humans
  • Infant
  • Male
  • Rhabdomyoma / complications
  • Rhabdomyoma / diagnostic imaging*
  • Rhabdomyoma / surgery
  • Treatment Outcome
  • Ultrasonography, Prenatal
  • Ventricular Outflow Obstruction / diagnostic imaging*
  • Ventricular Outflow Obstruction / etiology
  • Ventricular Outflow Obstruction / surgery