Hodgkin lymphoma in a patient with mosaic trisomy 18: First clinical observation

Am J Med Genet A. 2016 Mar;170(3):777-80. doi: 10.1002/ajmg.a.37504. Epub 2015 Dec 24.

Abstract

We report the case of a 17-year-old boy with a mosaic trisomy 18, who was diagnosed with Hodgkin lymphoma. The patient showed only poor growth and two muscular ventricular septal defects; no facial dysmorphims were present. He was admitted to our hospital because of asthenia and weight loss; a mediastinal enlargement was found and an histological diagnosis of nodular sclerosis Hodgkin lymphoma on mediastinal biopsy was performed. Contextually, a chromosomal analysis on bone marrow aspirate and on peripheral blood revealed a mosaic trisomy 18. This result was confirmed also with cytogenetic analysis on skin fibroblasts. While there is a well-documented association between trisomy 18 and solid cell tumors, this is, to our knowledge, the first reported case of Hodgkin lymphoma in a patient with a mosaic trisomy 18, enlarging the spectrum of possible oncologic manifestations of the disease.

Keywords: Hodgkin lymphoma; mosaic trisomy 18.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / diagnosis
  • Abnormalities, Multiple / genetics
  • Adolescent
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Chromosomes, Human, Pair 18 / genetics
  • Cyclophosphamide / therapeutic use
  • Hodgkin Disease / diagnosis*
  • Hodgkin Disease / drug therapy
  • Hodgkin Disease / etiology*
  • Humans
  • In Situ Hybridization, Fluorescence
  • Karyotyping
  • Male
  • Mosaicism*
  • Phenotype
  • Prednisone / therapeutic use
  • Procarbazine / therapeutic use
  • Treatment Outcome
  • Trisomy / diagnosis*
  • Trisomy / genetics*
  • Trisomy 18 Syndrome
  • Vincristine / therapeutic use

Substances

  • Procarbazine
  • Vincristine
  • Cyclophosphamide
  • Prednisone

Supplementary concepts

  • COPP protocol