Aortopulmonary window (APW) is a rare congenital malformation. It results from an incomplete division between the ascending aorta and the pulmonary artery. We describe a 26-year-old male, who presented with a grade II exertional dyspnea and palpitations. Echocardiography revealed an APW with an ascending aorta aneurysm. He underwent surgery under cardiopulmonary bypass without aortic cross-clamping. The APW was closed via the pulmonary artery flap technique using an autologous pericardial patch, and the aneurysm was repaired through the reduction aortoplasty technique. The patient was discharged on the 4(th) postoperative day. At 2 years' follow-up, he had remained asymptomatic and echocardiography showed aortic valve competence, ascending aorta diameter of 38 mm, and no residual shunt.
Keywords: Aneurysm; Aorta; Aortopulmonary septal defect; Heart defects; congenital.