Intravenous leiomyomatosis with intracardiac extension: an unusual presentation of uterine leiomyoma and evaluation with 256-slice dual-source multidetector CT and cardiac MRI

BMJ Case Rep. 2015 Dec 7:2015:bcr2015211712. doi: 10.1136/bcr-2015-211712.

Abstract

We report a case of a 40-year-old woman who presented with breathlessness, palpitations and vague pelvic pain for 6 months. The dyspnoea was non-exertional and episodic. She was a non-diabetic, non-hypertensive and had no history of prior surgeries. ECG and chest radiograph were normal. Cardiac MRI and 256-slice dual-source multidetector CT evaluation revealed the presence of a uterine and left adnexal mass with intravenous extension into the inferior vena cava via the gonadal veins, and further cephalad extension into the right atrium and ventricle. The patient was referred to the cardiothoracic surgery department and underwent two-stage surgical procedures. The first stage consisted of thoracotomy and tumour removal from the right atrium and inferior vena cava. In the second stage, hysterectomy and bilateral salpingo-oophorectomy was performed. The histological analysis of the excised specimen was consistent with an intravascular leiomyoma.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Dyspnea / etiology
  • Female
  • Heart Neoplasms / diagnosis*
  • Heart Neoplasms / pathology
  • Heart Neoplasms / surgery
  • Humans
  • Hysterectomy
  • Image Interpretation, Computer-Assisted
  • Leiomyomatosis / diagnosis*
  • Leiomyomatosis / pathology
  • Leiomyomatosis / surgery
  • Magnetic Resonance Imaging*
  • Multidetector Computed Tomography*
  • Ovariectomy
  • Pelvic Pain / etiology
  • Salpingostomy
  • Treatment Outcome
  • Uterine Neoplasms / diagnosis*
  • Uterine Neoplasms / pathology
  • Uterine Neoplasms / surgery
  • Vascular Neoplasms / diagnosis*
  • Vascular Neoplasms / pathology
  • Vascular Neoplasms / surgery
  • Vena Cava, Inferior / pathology*