Elevated transpulmonary gradient and cardiac magnetic resonance-derived right ventricular remodeling predict poor outcomes in sickle cell disease

Haematologica. 2016 Feb;101(2):e40-3. doi: 10.3324/haematol.2015.125229. Epub 2015 Nov 20.
No abstract available

Keywords: cardiomyopathy; magnetic resonance imaging; pulmonary hypertension; right ventricle; sickle cell disease.

Publication types

  • Clinical Trial
  • Letter
  • Research Support, N.I.H., Extramural

MeSH terms

  • Adult
  • Anemia, Sickle Cell / complications
  • Anemia, Sickle Cell / diagnosis*
  • Anemia, Sickle Cell / mortality
  • Anemia, Sickle Cell / pathology
  • Cardiac Catheterization
  • Cardiac Output
  • Cardiac Volume
  • Female
  • Heart Rate
  • Humans
  • Hypertension, Pulmonary / complications
  • Hypertension, Pulmonary / diagnosis*
  • Hypertension, Pulmonary / mortality
  • Hypertension, Pulmonary / pathology
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Survival Analysis
  • Vascular Resistance*
  • Ventricular Function, Right
  • Ventricular Remodeling*

Associated data

  • ClinicalTrials.gov/NCT00011648
  • ClinicalTrials.gov/NCT00023296
  • ClinicalTrials.gov/NCT00081523
  • ClinicalTrials.gov/NCT00352430