Mondini dysplasia with recurrent bacterial meningitis caused by three different pathogens

Pediatr Int. 2015 Dec;57(6):1192-5. doi: 10.1111/ped.12731. Epub 2015 Nov 5.

Abstract

Mondini dysplasia is rare, but has an important association with recurrent bacterial meningitis. We herein describe the case of a 3-year-old girl with unilateral sensorineural hearing loss who presented with three independent episodes of bacterial meningitis within 8 months. Temporal bone computed tomography indicated the characteristic features of Mondini dysplasia in the right inner ear. This was treated by surgical closure of the inner ear defect via oval window and additional vaccination was administered. Appropriate vaccination might prevent the recurrent bacterial meningitis associated with Mondini dysplasia.

Keywords: Mondini dysplasia; anomaly; bacterial meningitis; immunodeficiency; pneumococcal vaccine.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Bacteria / isolation & purification*
  • Child, Preschool
  • Female
  • Hearing Loss, Sensorineural / complications*
  • Hearing Loss, Sensorineural / diagnosis
  • Histiocytosis, Langerhans-Cell / complications*
  • Histiocytosis, Langerhans-Cell / diagnosis
  • Humans
  • Immunocompromised Host*
  • Meningitis, Bacterial / complications*
  • Meningitis, Bacterial / diagnosis
  • Meningitis, Bacterial / microbiology
  • Tomography, X-Ray Computed