Rapp-Hodgkin syndrome: an ectodermal dysplasia involving the teeth, hair, nails, and palate. Report of a case and review of the literature

P J Crawford; M J Aldred; A Clarke; M S Tso

doi:10.1016/0030-4220(89)90302-2

Rapp-Hodgkin syndrome: an ectodermal dysplasia involving the teeth, hair, nails, and palate. Report of a case and review of the literature

Oral Surg Oral Med Oral Pathol. 1989 Jan;67(1):50-62. doi: 10.1016/0030-4220(89)90302-2.

Authors

P J Crawford¹, M J Aldred, A Clarke, M S Tso

Affiliation

¹ Department of Child Dental Health, University of Wales College of Medicine, Cardiff, United Kingdom.

PMID: 2643072
DOI: 10.1016/0030-4220(89)90302-2

Abstract

Rapp-Hodgkin syndrome is a rare form of ectodermal dysplasia involving the hair, eyes, sweat glands, nails, teeth, and palate. The case of a white girl with the condition is presented. The differential diagnosis is discussed, and the eight previously reported cases are reviewed. Another (ninth) previously reported case is considered for inclusion in the group.

Publication types

Case Reports
Review

MeSH terms

Child, Preschool
Diagnosis, Differential
Ectodermal Dysplasia / pathology*
Female
Humans
Palate / pathology*
Skin Diseases / pathology*
Syndrome
Tooth Abnormalities / pathology*