Cardiac Involvement in a Patient With POEMS Syndrome Detected Using Cardiac Magnetic Resonance Imaging

Int Heart J. 2015;56(5):571-3. doi: 10.1536/ihj.15-038. Epub 2015 Sep 4.

Abstract

We present a case of POEMS syndrome in which cardiac MRI (CMR) revealed cardiac involvement. POEMS syndrome is a very rare disease and cardiac involvement in POEMS syndrome is rarely reported. In the present case, echocardiography revealed left ventricular hypertrophy with moderately impaired systolic function and moderate pulmonary hypertension. CMR examination showed a typical circular subendocardial type of late gadolinium enhancement, which is a classic pattern of cardiac amyloidosis. The diagnosis of cardiac amyloidosis in POEMS would be helpful for further risk stratification and treatment strategies.

Publication types

  • Case Reports

MeSH terms

  • Amyloidosis* / complications
  • Amyloidosis* / diagnosis
  • Amyloidosis* / physiopathology
  • Biopsy
  • Diagnosis, Differential
  • Disease Management
  • Echocardiography / methods
  • Electrocardiography / methods
  • Female
  • Gadolinium / pharmacology*
  • Humans
  • Hypertension, Pulmonary / diagnosis
  • Hypertension, Pulmonary / etiology
  • Hypertension, Pulmonary / physiopathology
  • Hypertrophy, Left Ventricular* / complications
  • Hypertrophy, Left Ventricular* / diagnostic imaging
  • Hypertrophy, Left Ventricular* / physiopathology
  • Image Enhancement / methods
  • Magnetic Resonance Imaging / methods
  • Middle Aged
  • POEMS Syndrome* / complications
  • POEMS Syndrome* / diagnosis
  • POEMS Syndrome* / physiopathology
  • Radiography
  • Radiopharmaceuticals / pharmacology
  • Ventricular Dysfunction, Left / diagnosis
  • Ventricular Dysfunction, Left / etiology
  • Ventricular Dysfunction, Left / physiopathology

Substances

  • Radiopharmaceuticals
  • Gadolinium