Pseudotumoral Behçet's disease

Reumatol Clin. 2016 Mar-Apr;12(2):85-90. doi: 10.1016/j.reuma.2015.03.007. Epub 2015 Jun 13.
[Article in English, Spanish]

Abstract

Behçet's disease is a systemic vasculitis characterized by the presence of oral and genital ulcers. Neurological involvement or neuro-Behçet is an uncommon manifestation. It manifestation has predominance in the male gender appearing 2 to 4 years after the first clinical manifestation. However, neuro-Behçet disease sometimes occurs with pseudotumoral brain lesions. Herein, we present the cases of two patients diagnosed with neuro-Behçet after detection of pseudotumoral brain lesions. A review of the literature is performed.

Keywords: Behçets disease; Enfermedad de Behçet; Lesiones cerebrales pseudotumorales; Neuro-Behçet; Neuro-Behçets disease; Pseudotumotal brain lesions.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Behcet Syndrome / diagnosis*
  • Brain Diseases / diagnosis*
  • Female
  • Humans
  • Male
  • Middle Aged