Objective: To report the clinical and pathologic features of an elderly patient with a unilateral orbital swelling and proptosis caused by Juvenile Xanthogranuloma diagnosed and confirmed by orbital biopsy.
Design: Interventional case report.
Participants: One patient.
Intervention: Steroids (Medrol dose pack) and radiation.
Main outcome measures: Unusual clinical presentation and pathological features of Juvenile Xanthogranuloma in the orbit.
Conclusions: Juvenile Xanthogranuloma affecting one orbit is very rare with unilateral involvement in an elderly patient. Steroids and radiation therapy were very effective in treatment and provided impressive results.
Keywords: Elderly; Juvenile Xanthogranuloma; orbital.