[Renal amyloidosis revealing a Kartagener's syndrome]

Nephrol Ther. 2015 Feb;11(1):50-2. doi: 10.1016/j.nephro.2014.09.003. Epub 2014 Nov 28.
[Article in French]

Abstract

Kartagener's syndrome is a rare disease. It is a clinical variant of primary ciliary dyskinesia. It combines a situs inversus, chronic sinusitis and bronchiectasis. Glomerulopathies associated with this syndrome are rarely reported. We report the case of Kartagener's syndrome in a patient diagnosed at the age of 37 years with renal amyloidosis.

Keywords: Amylose rénale; Bronchectasie; Bronchiectasis; Kartagener's syndrome; Renal amyloidosis; Syndrome de Kartagener.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Amyloidosis / etiology*
  • Female
  • Humans
  • Kartagener Syndrome / diagnosis*
  • Kidney Diseases / etiology*
  • Male