Orbital lymphomatoid granulomatosis - a rare cause of proptosis

Jacqueline du Toit; Tracy Kilborn; Ann Van Eyssen; Komala Pillay

doi:10.1007/s00247-014-3206-7

Orbital lymphomatoid granulomatosis - a rare cause of proptosis

Pediatr Radiol. 2015 Jul;45(7):1095-8. doi: 10.1007/s00247-014-3206-7. Epub 2014 Nov 8.

Authors

Jacqueline du Toit¹, Tracy Kilborn, Ann Van Eyssen, Komala Pillay

Affiliation

¹ Department of Radiology, Red Cross Children's Hospital, Private Bag X5, Rondebosch, 7700, South Africa, jacqueline.dut@googlemail.com.

PMID: 25381000
DOI: 10.1007/s00247-014-3206-7

Abstract

A 1-year-old girl with unilateral proptosis was found to have primary orbital lymphomatoid granulomatosis - a condition rarely occurring in children. This multisystem angiocentric, angiodestructive, lymphoproliferative disease typically involves the lungs, with ocular involvement being extremely uncommon. Our case serves to illustrate the imaging findings of this unusual condition and highlight a rare cause of proptosis.

Publication types

Case Reports

MeSH terms

Diagnosis, Differential
Exophthalmos / drug therapy
Exophthalmos / etiology*
Exophthalmos / pathology*
Female
Humans
Infant
Lymphomatoid Granulomatosis / complications*
Lymphomatoid Granulomatosis / drug therapy
Lymphomatoid Granulomatosis / pathology*
Magnetic Resonance Imaging
Orbit / pathology
Orbital Neoplasms / complications*
Orbital Neoplasms / drug therapy
Orbital Neoplasms / pathology*
Rare Diseases