Purpose: To report a case of systemic lupus erythematosus vaso-occlusive retinopathy illustrating vascular remodeling over 4 years of follow-up.
Methods: Observational case report of one patient.
Results: A 12-year-old previously healthy girl presented with profound vision loss to 20/800 in both eyes. Her medical workup, neuro-imaging, and ophthalmic examination were consistent with coexistent central nervous system systemic lupus erythematosus and vaso-occlusive systemic lupus erythematosus retinopathy. At 15 months after presentation, retinal vasculature remodeling was evident along with severe macular atrophy. By 4 years after presentation, retinal neovascularization developed that was successfully treated with photocoagulation.
Conclusion: We describe a case of systemic lupus erythematosus vaso-occlusive retinopathy illustrating vascular remodeling over 4 years of follow-up.