Primary biliary cirrhosis (PBC) is an autoimmune, chronic, cholestatic liver disease that affects primarily women. PBC is commonly associated with hypercholesterolemia that has been associated with cholestasis. We report an exceptionally high blood cholesterol and phytosterols with just mild cholestasis indicating a selective defect in sterol biliary secretion in a patient with PBC.
Keywords: Hypercholesterolemia; Phytosterolemia; Primary biliary cirrhosis; Xanthomas.
Copyright © 2014 National Lipid Association. Published by Elsevier Inc. All rights reserved.