Complement membrane attack complex is related with immune-mediated necrotizing myopathy

Int J Clin Exp Pathol. 2014 Jun 15;7(7):4143-9. eCollection 2014.

Abstract

This study is to investigate the expression of complement membrane attack complex (C5b-9) in the skeletal muscle of patients with necrotizing myopathy (NM), and to investigate the relationship between C5b-9 and NM. Thirteen patients with NM and control patients with polymyositis and muscular dystrophy were enrolled in this study. Examinations including creatine kinase (CK) and L-lactate dehydrogenase (LDH) in the serum, electromyogram and muscle pathological examination were performed. C5b-9 expression in the skeletal muscle was determined by immunohistochemistry and analyzed by Image Plus Pro 6.0. C5b-9 expression was particularly prominent in necrotic muscle fibers, and also positive in blood vessels. C5b-9 diffusely expressed in vascular endothelial cells and smooth muscle layer. But the intensity was not related with the elevated level of serum CK. So, C5b-9 is strongly expressed in the necrotic muscle fiber and blood vessels, and may contribute to the pathogenesis of NM.

Keywords: C5b-9; Necrotizing myopathy; complement membrane attack complex; endothelial cell; muscle fiber.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Child
  • Complement Membrane Attack Complex / analysis
  • Complement Membrane Attack Complex / immunology*
  • Female
  • Humans
  • Immunohistochemistry
  • Male
  • Middle Aged
  • Muscle, Skeletal / immunology
  • Muscle, Skeletal / pathology*
  • Muscular Diseases / immunology*
  • Muscular Diseases / pathology*
  • Necrosis
  • Young Adult

Substances

  • Complement Membrane Attack Complex