[Eosinophilic granulomatosis with polyangiitis presenting as livedo racemosa]

Hautarzt. 2014 Apr;65(4):276-9. doi: 10.1007/s00105-014-2785-4.
[Article in German]

Abstract

As a rare antineutrophil cytoplasmic antibodies (ANCA)-associated vasculitis, eosinophilic granulomatosis with polyangiitis (EGPA, formerly Churg-Strauss syndrome) is characterized by asthma, severe peripheral eosinophilia and the presence of extravascular granulomas. Cutaneous involvement usually includes palpable purpura or cutaneous to subcutaneous nodes. We present the case of a 43-year-old woman with EPGA and the unusual cutaneous manifestation of livedo racemosa.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Anti-Inflammatory Agents / therapeutic use
  • Churg-Strauss Syndrome / diagnosis*
  • Churg-Strauss Syndrome / drug therapy
  • Diagnosis, Differential
  • Female
  • Granulomatosis with Polyangiitis / diagnosis*
  • Granulomatosis with Polyangiitis / drug therapy
  • Humans
  • Livedo Reticularis / diagnosis*
  • Livedo Reticularis / drug therapy
  • Treatment Outcome

Substances

  • Anti-Inflammatory Agents