Abstract
The paper gives data on the prevalence of arrhythmogenic right ventricular cardiomyopathy/dysplasia as one of the common causes of sudden cardiac death, achievements in its molecular genetics, possible causes and cause-and-effect relations, microscopic and morphometric features of diagnosis.
MeSH terms
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Arrhythmogenic Right Ventricular Dysplasia / diagnosis*
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Arrhythmogenic Right Ventricular Dysplasia / genetics
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Arrhythmogenic Right Ventricular Dysplasia / mortality
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Arrhythmogenic Right Ventricular Dysplasia / physiopathology*
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Death, Sudden, Cardiac / etiology
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Death, Sudden, Cardiac / pathology*
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Heart Rate
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Humans
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Myocardium / metabolism
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Myocardium / pathology
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Myocardium / ultrastructure*