Fertility sparing treatment of a malignant uterine perivascular epithelioid cell tumor: A case report

Gynecol Oncol Case Rep. 2014 Jan 22:8:14-6. doi: 10.1016/j.gynor.2014.01.001. eCollection 2014 Apr.

Abstract

•Perivascular epithelioid cell tumors (PEComas) are a family of rare, poorly defined mesenchymal tumors of uncertain malignant potential.•Treatment for PEComas has most commonly involved excisional biopsy or surgical resection.•The use of mTOR inhibitors may provide the best medical treatment as well as a fertility-sparing treatment option.

Keywords: Chemotherapy; Perivascular epithelioid cell tumor; Uterine neoplasm; mTOR inhibitor.