Pediatric Cone-Rod Dystrophy with High Myopia and Nystagmus Suggests Recessive PROM1 Mutations

Ophthalmic Genet. 2015;36(4):349-52. doi: 10.3109/13816810.2014.886266. Epub 2014 Feb 18.

Abstract

Pediatric cone-rod dystrophies are a genetically heterogenous group of disorders characterized by photophobia, progressive loss of central vision, and subsequent gradual loss of peripheral vision. In general, clinical presentation is not specific for a particular gene mutation; however, there are exceptions, which are important to recognize in order to facilitate molecular diagnosis. In this report, we highlight that pediatric cone-rod dystrophy with high myopia and nystagmus suggests recessive mutations in the gene PROM1.

Keywords: Cone-rod dystrophy; PROM1; high myopia; nystagmus.

Publication types

  • Case Reports

MeSH terms

  • AC133 Antigen
  • Antigens, CD / genetics*
  • Female
  • Fluorescein Angiography
  • Genes, Recessive
  • Glycoproteins / genetics*
  • Humans
  • Mutation*
  • Myopia, Degenerative / diagnosis
  • Myopia, Degenerative / genetics*
  • Nystagmus, Pathologic / diagnosis
  • Nystagmus, Pathologic / genetics*
  • Peptides / genetics*
  • Retinitis Pigmentosa / diagnosis
  • Retinitis Pigmentosa / genetics*
  • Tomography, Optical Coherence
  • Young Adult

Substances

  • AC133 Antigen
  • Antigens, CD
  • Glycoproteins
  • PROM1 protein, human
  • Peptides