Cardiac involvement in antiphospholipid syndrome associated with Sneddon syndrome: a challenging diagnosis

Rev Port Cardiol. 2014 Feb;33(2):115.e1-7. doi: 10.1016/j.repc.2013.09.006. Epub 2014 Feb 7.
[Article in English, Portuguese]

Abstract

Sneddon syndrome is a rare clinical entity characterized by the association of ischemic cerebrovascular disease and livedo reticularis. The authors report a case of stroke and myocardial infarction in a 39-year-old man with Sneddon syndrome and antiphospholipid syndrome who subsequently met some criteria for systemic lupus erythematosus, highlighting the complexity of cardiovascular involvement in systemic diseases.

Keywords: Acidente vascular cerebral; Antiphospholipid syndrome; Enfarte agudo do miocárdio; Livedo reticularis; Lúpus eritematoso sistémico; Myocardial infarction; Sneddon syndrome; Stroke; Systemic lupus erythematosus; Síndroma antifosfolipídica; Síndroma de Sneddon.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Antiphospholipid Syndrome / complications*
  • Humans
  • Male
  • Myocardial Infarction / etiology*
  • Sneddon Syndrome / complications*
  • Stroke / etiology*