Ruptured subscapular artery aneurysm and subclavian artery occlusion in a patient with type 1 neurofibromatosis: a case report

J Med Case Rep. 2014 Feb 5:8:39. doi: 10.1186/1752-1947-8-39.

Abstract

Introduction: Collateral muscular artery aneurysm is exceedingly rare. We report the first case of subscapular artery aneurysm in a patient with type 1 neurofibromatosis and ipsilateral chronic subclavian artery occlusion.

Case presentation: A 74-year-old Caucasian woman with a medical history of type 1 neurofibromatosis, presented a sudden left pectoral mass, later diagnosed as a ruptured aneurysm of the left subscapular artery. It was caused by a chronic occlusion of the left subclavian artery, diagnosed on angiographies prior to embolization.

Conclusions: Collateral artery aneurysm in the event of a mainstream muscular artery chronic occlusion may occur in type 1 neurofibromatosis.