Unruptured translabyrinthine meningocele without CSF otorrhea

Int J Pediatr Otorhinolaryngol. 2014 Mar;78(3):566-9. doi: 10.1016/j.ijporl.2013.12.034. Epub 2014 Jan 10.

Abstract

Labyrinthine meningocele can be classified into translabyrinthine and perilabyrinthine type. We describe a case of rare unruptured translabyrinthine meningocele (TLM). It is rare to encounter an unruptured TLM because it is usually diagnosed after rupture as a labyrinthine fistula, cerebral spinal fluid otorrhea, and subsequent meningitis. We provide for the first time an intraoperative photo and video of a case of an unruptured TLM that developed through an inner ear malformation in a single-side deaf child, which was preoperatively misdiagnosed as congenital cholesteatoma in preoperative temporal bone computed tomography. TLM without CSF otorrhea in an unruptured state merit attention because of its importance during the workup of congenital cholesteatoma or cochlear implantation in spite of its rarity of reports.

Keywords: CSF otorrhea; Congenital malformation; Labyrinthine meningocele.

Publication types

  • Case Reports

MeSH terms

  • Cerebrospinal Fluid Otorrhea / diagnosis*
  • Child
  • Cholesteatoma / congenital*
  • Cholesteatoma / diagnosis
  • Cholesteatoma / surgery
  • Cholesteatoma, Middle Ear / diagnosis*
  • Cholesteatoma, Middle Ear / surgery
  • Deafness / diagnosis
  • Deafness / surgery
  • Diagnosis, Differential
  • Ear, Inner / abnormalities*
  • Female
  • Humans
  • Magnetic Resonance Imaging / methods
  • Meningocele / diagnosis*
  • Meningocele / surgery
  • Otologic Surgical Procedures / methods
  • Rare Diseases
  • Risk Assessment
  • Severity of Illness Index
  • Surgical Flaps
  • Tomography, X-Ray Computed / methods
  • Treatment Outcome

Supplementary concepts

  • Cholesteatoma, Congenital