Cor triatriatum dexter, atrial septal defects, and pulmonary stenosis-a rare association

Echocardiography. 2014 Apr;31(4):E124-7. doi: 10.1111/echo.12516. Epub 2014 Jan 22.

Abstract

Cor triatriatum dexter (CTD) is an extremely rare congenital anomaly in which the right atrium is divided into 2 chambers by a membrane. The estimated incidence of cor triatriatum has been reported as 0.1% of congenital cardiac malformations. The septation of the right atrium in the setting of CTD is the result of failed resorption of the right valve of the sinus venosus. This results in anterolateral and posteromedial portions of the divided right atrium. CTD can be diagnosed at any age, especially if it is incidentally discovered.

Keywords: atrial septal defect; congenital heart disease; cor triatriatum dexter; echocardiography; pulmonary stenosis.

Publication types

  • Case Reports

MeSH terms

  • Cor Triatriatum / complications
  • Cor Triatriatum / diagnosis
  • Cor Triatriatum / diagnostic imaging*
  • Echocardiography / methods
  • Electrocardiography / methods
  • Female
  • Heart Atria / abnormalities
  • Heart Atria / diagnostic imaging*
  • Heart Septal Defects, Atrial / complications
  • Heart Septal Defects, Atrial / diagnosis
  • Heart Septal Defects, Atrial / diagnostic imaging*
  • Humans
  • Multimodal Imaging / methods
  • Pulmonary Valve Stenosis / complications
  • Pulmonary Valve Stenosis / diagnosis
  • Pulmonary Valve Stenosis / diagnostic imaging*
  • Rare Diseases
  • Tomography, X-Ray Computed / methods
  • Young Adult