Intracranial fibromuscular dysplasia presenting as various ocular manifestations

Abstract

Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory vascular disease that mainly affects renal, extracranial carotid, and vertebral arteries. Intracranial FMD is uncommon unlike extracranial or renal FMD, and the primary manifestation of intracranial FMD is intracranial aneurysm. We report an unusual case of intracranial FMD showing various ocular manifestations, including central retinal artery occlusion, transient monocular blindness, and oculomotor nerve palsy without renal involvement.

Keywords: Brian stem infarct; Central retinal artery occlusion; Fibromuscular dysplasia; Oculomotor never palsy; String of bead; Transient visual loss.