Parry-Romberg syndrome with rare maxillofacial deformities: a report on two cases

J Craniomaxillofac Surg. 2014 Sep;42(6):780-3. doi: 10.1016/j.jcms.2013.11.010. Epub 2013 Nov 26.

Abstract

Parry-Romberg syndrome, also known as progressive hemifacial atrophy, is a rare developmental disorder characterized by progressing unilateral facial atrophy slowly, which may affect the skin, fat, muscle and bone. It can also be associated with different systemic manifestations and deformities. In this article, we present the two cases with Parry-Romberg syndrome. Of them, one has additional and rare facial deformity with rare facial cleft and the other has a special tongue feature.

Keywords: Facial cleft; Parry–Romberg syndrome; Tongue deformity.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Cleft Palate / diagnosis
  • Facial Bones / abnormalities*
  • Facial Hemiatrophy / diagnosis*
  • Humans
  • Male
  • Maxilla / abnormalities
  • Maxillary Sinus / abnormalities
  • Nasal Bone / abnormalities
  • Tongue / abnormalities*
  • Zygoma / abnormalities