We report on a meningioma of the cervical spine in a 12-year-old boy with atypical clinical presentation. Meningiomas are relatively rare neoplasms in childhood, representing only 1 to 2% of all pediatric intracranial tumors. The distinction between the meningioma and another extramedullary, intradural tumors like schwannoma might pose difficulties. This case report points out that although a very rare tumor in children, it must be taken into account in differential diagnostics.