Targeted therapies in rare sarcomas: IMT, ASPS, SFT, PEComa, and CCS

Abstract

This article highlights the data currently available on the activity of targeted medical treatment in a subgroup of rare entities within soft tissue sarcomas, including inflammatory myofibroblastic tumor, alveolar soft part sarcoma, solitary fibrous tumor, malignant perivascular epithelioid cell tumor (PEComa), and clear cell sarcoma.

Keywords: Alveolar soft part sarcoma; Chemotherapy; Clear cell sarcoma; Hemangiopericytoma; Inflammatory myofibroblastic tumor; Perivascular epithelioid cell tumor; Sarcoma; Solitary fibrous tumor.