Pneumomediastinum and hyponatraemic dehydration as presenting features of cystic fibrosis

Eur Respir J. 2013 Dec;42(6):1760-2. doi: 10.1183/09031936.00124713. Epub 2013 Sep 26.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Child
  • Cough
  • Cystic Fibrosis / complications*
  • Cystic Fibrosis / diagnosis*
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Dehydration / complications
  • Dehydration / diagnosis*
  • Female
  • Humans
  • Hyponatremia / complications
  • Hyponatremia / diagnosis*
  • Male
  • Mediastinal Emphysema / complications
  • Mediastinal Emphysema / diagnosis*
  • Radiography, Thoracic
  • Siblings
  • Tomography, X-Ray Computed
  • United Kingdom

Substances

  • CFTR protein, human
  • Cystic Fibrosis Transmembrane Conductance Regulator