Pancreatic neuroendocrine tumor with ectopic adrenocorticotropin production: a case report and review of literature

Anticancer Res. 2013 Sep;33(9):4001-5.

Abstract

Pancreatic neuroendocrine tumors (p-NETs) entail a vast array of tumors, which can vary from benign neoplastic growths to rapidly aggressive malignancies. Such is the case with ectopic adrenocorticotropic hormone (ACTH)-producing p-NETs. These tumors have been found to be quite aggressive and a challenge to treat, especially due to the occurrence of metastatic disease even after resection of the primary tumor. We discuss the case of a 44-year-old female who initially presented with vague, non-specific symptoms, in which a malignant p-NET was found to be the cause of her clinical presentation. Although resection of the pancreatic mass was performed, the patient presented again with metastatic disease to the liver.

Keywords: Cushing's Syndrome; Pancreatic neuroendocrine tumor; ectopic ACTH syndrome; gastroenteropancreatic neuroendocrine tumor.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adrenocorticotropic Hormone / biosynthesis*
  • Adult
  • Antineoplastic Agents, Hormonal / therapeutic use
  • Female
  • Humans
  • Neuroendocrine Tumors / diagnosis*
  • Neuroendocrine Tumors / drug therapy
  • Neuroendocrine Tumors / metabolism
  • Neuroendocrine Tumors / pathology
  • Octreotide / therapeutic use
  • Pancreatic Neoplasms / diagnosis*
  • Pancreatic Neoplasms / drug therapy
  • Pancreatic Neoplasms / metabolism
  • Pancreatic Neoplasms / pathology

Substances

  • Antineoplastic Agents, Hormonal
  • Adrenocorticotropic Hormone
  • Octreotide