Nucleolar control of p53: a cellular Achilles' heel and a target for cancer therapy

Cell Mol Life Sci. 2014 Mar;71(5):771-91. doi: 10.1007/s00018-013-1361-x. Epub 2013 May 18.

Abstract

Nucleoli perform a crucial cell function, ribosome biogenesis, and of critical relevance to the subject of this review, they are also extremely sensitive to cellular stresses, which can cause loss of function and/or associated structural disruption. In recent years, we have learned that cells take advantage of this stress sensitivity of nucleoli, using them as stress sensors. One major protein regulated by this role of nucleoli is the tumor suppressor p53, which is activated in response to diverse cellular injuries in order to exert its onco-protective effects. Here we discuss a model of nucleolar regulation of p53, which proposes that key steps in the promotion of p53 degradation by the ubiquitin ligase MDM2 occur in nucleoli, thus providing an explanation for the observed link between nucleolar disruption and p53 stability. We review current evidence for this compartmentalization in p53 homeostasis and highlight current limitations of the model. Interestingly, a number of current chemotherapeutic agents capable of inducing a p53 response are likely to do so by targeting nucleolar functions and these compounds may serve to inform further improved therapeutic targeting of nucleoli.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Cell Nucleolus / metabolism
  • Cell Nucleolus / physiology*
  • Gene Expression Regulation, Neoplastic / genetics*
  • Models, Biological*
  • Neoplasms / metabolism
  • Neoplasms / physiopathology*
  • Protein Stability
  • Protein Transport / physiology
  • Proteolysis*
  • Proto-Oncogene Proteins c-mdm2 / metabolism
  • Ribosomes / metabolism
  • Stress, Physiological / physiology*
  • Tumor Suppressor Protein p53 / metabolism*

Substances

  • Tumor Suppressor Protein p53
  • Proto-Oncogene Proteins c-mdm2