Transverse-sigmoid sinus dural arteriovenous fistula presenting with parkinsonism

Neurol Med Chir (Tokyo). 2013;53(4):224-7. doi: 10.2176/nmc.53.224.

Abstract

Dural arteriovenous fistula (DAVF) is rarely associated with parkinsonism. A 52-year-old woman presented with a rare case of DAVF manifesting as parkinsonism and subsequently akinetic mutism. She showed dramatic recovery after endovascular treatment. We also review 10 published reports of DAVF presenting with parkinsonism. The clinical features of these cases at presentation was more closely compatible with lower body parkinsonism or vascular parkinsonism rather than Parkinson's disease. Most lesions are located at the transverse-sigmoid sinus (TSS) with venous reflux into the straight sinus with probable venous congestion of the basal ganglia. Most importantly, parkinsonism due to TSS DAVF is reversible if embolization is achieved successfully.

Publication types

  • Review

MeSH terms

  • Central Nervous System Vascular Malformations / complications*
  • Central Nervous System Vascular Malformations / diagnosis
  • Central Nervous System Vascular Malformations / therapy
  • Cerebral Angiography
  • Cranial Sinuses / pathology
  • Diagnosis, Differential
  • Diffusion Magnetic Resonance Imaging
  • Embolization, Therapeutic
  • Female
  • Follow-Up Studies
  • Humans
  • Magnetic Resonance Imaging
  • Middle Aged
  • Neurologic Examination
  • Parkinsonian Disorders / diagnosis
  • Parkinsonian Disorders / etiology*
  • Parkinsonian Disorders / therapy
  • Tomography, X-Ray Computed
  • Transverse Sinuses* / abnormalities
  • Transverse Sinuses* / pathology