Malignant schwannoma in the naso-maxillary region is very rare. Only 20 eases have been reported in the literature (Maheshwari et al 99) Melanotic variety of this tumor is extremely rare and only 4 cases have been found in internet search. Surgery followed by radiotherapy has been advocated for treatment. A case is reported involving maxilla in a 13 year old female patient because of its extreme rarity. The case was treated by surgery and showed no recurrence during a 3 year follow-up period.
Keywords: Malignant Schwannoma; Maxilla.