Mid-aortic syndrome in a 3-year-old girl successfully treated by aorto-aortic grafting and renal artery implantation into the graft

Tex Heart Inst J. 2012;39(5):657-61.

Abstract

Mid-aortic syndrome, an uncommon acquired or congenital condition characterized by segmental narrowing of the abdominal or distal descending thoracic aorta, is frequently accompanied by ostial stenosis of the aorta's branches. If left untreated, it can result in life-threatening complications secondary to severe hypertension.We report the case of a 3-year-old girl with congenital mid-aortic syndrome, who was diagnosed by chance in the course of a viral illness, and whose high blood pressure values were first dismissed as inaccurate. Attempts to achieve medical or endovascular control of her hypertension were unsuccessful. She was thereafter successfully treated by aorto-aortic bypass grafting, resection of the stenotic segments of both renal arteries, and implantation of the patent arterial segments into the graft.

Keywords: Angioplasty, balloon; aorta, abdominal/abnormalities; aortic coarctation/etiology/surgery; arterial occlusive diseases/surgery; child; hypertension, renal/etiology/surgery; mid-aortic syndrome; reconstructive surgical procedures/methods; renal artery obstruction/surgery.

Publication types

  • Case Reports
  • Video-Audio Media

MeSH terms

  • Aorta, Abdominal / abnormalities
  • Aorta, Abdominal / physiopathology
  • Aorta, Abdominal / surgery*
  • Aortic Diseases / congenital
  • Aortic Diseases / diagnosis
  • Aortic Diseases / physiopathology
  • Aortic Diseases / surgery*
  • Aortography
  • Blood Pressure
  • Blood Vessel Prosthesis Implantation / methods*
  • Child, Preschool
  • Constriction, Pathologic
  • Female
  • Humans
  • Hypertension, Renovascular / etiology
  • Hypertension, Renovascular / physiopathology
  • Hypertension, Renovascular / surgery
  • Incidental Findings
  • Magnetic Resonance Angiography
  • Renal Artery / abnormalities
  • Renal Artery / physiopathology
  • Renal Artery / surgery*
  • Renal Artery Obstruction / congenital
  • Renal Artery Obstruction / diagnosis
  • Renal Artery Obstruction / physiopathology
  • Renal Artery Obstruction / surgery*
  • Syndrome
  • Treatment Outcome